Cystic Fibrosis : Symptoms, Causes, Complication, Prevention and Treatment

Cystic Fibrosis : Symptoms, Causes, Complication, Prevention and Treatment

Cystic fibrosis is also known as mucoviscidosis. It is an inherited disorder which causes severe damage to the lungs, digestive system, and other organs in the body. Mucoviscidosis affects the cells which produce mucus, sweat, and digestive juices. These secreted fluids are normally thin and slippery.

See Also: Online Pharmacy India

In some people with cystic fibrosis, a defective gene causes the secretions to become sticky and thick.

Before acting as a lubricant, the secretions plug up tubes, ducts, and passageways, especially in the lungs, and pancreas.

See Also: Online pharmacy Delhi

What is Cystic Fibrosis?

It is a hereditary disorder which affects the exocrine glands. It causes the production of abnormally thick and broad mucus, leading to the blockage of the pancreatic ducts, intestines, and bronchi and often resulting in respiratory infection.

See Also: Online medicine store

What are the Symptoms of Cystic Fibrosis?

There are few symptoms ofďż˝ mucoviscidosis

Respiratory symptoms are :

1. A persistent cough that produces thick mucus 2. Wheezing 3. Breathlessness 4. Exercise intolerance 5. Repeated lung infections 6. Inflamed nasal passages or a stuffy nose

Digestive symptoms are:

1. Foul-smelling, greasy stools 2. Poor weight gain and growth 3. Intestinal blockage, particularly in newborns (meconium ileus) 4. Severe constipation

What are the Causes of Cystic Fibrosis?

There are some causes of cystic fibrosis:

In mucoviscidosis, a defect (mutation) in a gene changes a protein that regulates the movement of salt in and out of cells. As the result, the mucus gets thick and sticky in the respiratory, digestive and reproductive systems, as well as increased salt in sweat is found.

See Also: Medicine online purchase Many different defects can appear in the gene. This kind of gene mutation is associated with the severity of the condition.

What are the Risk Factors of Cystic Fibrosis?

There are mainly two risk factors ofďż˝ mucoviscidosis :

1. Family history It is an inherited disorder, it runs in families.

2. Race It occurs in all races, it is most common in white people of Northern European ancestry.

What are the Complications of Cystic Fibrosis?

There are few complications such as :

Respiratory system complications

Damaged airwaysďż˝

Cystic fibrosis is one of the leading causes of bronchiectasis, a condition that damages the airways. It makes harder to move air in and out of the lungs and clear mucus from the airways (bronchial tubes).

See Also: buy medicines Chronic infections:

Dense mucus in the lungs and sinuses provides an ideal breeding ground for bacteria and fungi. People with mucoviscidosis have sinus infections, bronchitis or pneumonia.

Growths in the nose Because the lining inside the nose is inflamed and swollen, it can develop soft, fleshy growths (polyps).

Coughing up bloodďż˝ Cystic fibrosis can cause thinning of the airway walls. As per the result, teenagers and adults with mucoviscidosis may cough up blood.

Pneumothorax: This condition when air collects in the space which separates the lungs from the chest wall is more common in older people with mucoviscidosis. It can cause chest pain and breathlessness.

See Also: online medicine delivery in delhi

Respiratory failure:

Cystic fibrosis can damage the lung tissue so badly that it no longer works. Lung function usually worsens gradually, and it eventually can become life-threatening.

Acute Exacerbations: People with mucoviscidosis may experience worsening of their respiratory symptoms, such as coughing and shortness of breath, for several days to weeks. It requires treatment in the hospital.

See Also: purchase medicine

Digestive system complications

Nutritional deficiencies

Thick mucus can block the tubes which carry digestive enzymes from your pancreas to your intestines.

As without these enzymes, your body can’t absorb protein, fats or fat-soluble vitamins.

Diabetes:

The pancreas makes insulin, which your body needs to use sugar. Mucoviscidosis increases the risk of diabetes. Around 30 % of people with mucoviscidosis develop diabetes by the age of 30-40.

Blocked bile duct: A tube which carries cattiness from your liver and gallbladder to your small intestine may become blocked and inflamed, leading to liver problems and sometimes gallstones.

Intestinal obstruction: It can happen to people with mucoviscidosis at all ages. Children and adults with cystic fibrosis are more likely than are infants to develop intussusception, a condition in which a section of the intestines folds in on itself like an accordion.

See Also: order medicine online Noida

Distal intestinal obstruction syndrome (DIOS) It is partial or complete obstruction where the small intestine meets the large intestine.

What are the Preventions?

There are some preventions ofďż˝ mucoviscidosis :

If you or your partner has close relatives with mucoviscidosis, you both want to undergo genetic testing before having children. The test, which is performed in a lab on a sample of blood, it can help to determine your risk of having a child with mucoviscidosis.

If you’re pregnant and the genetic test shows that your baby might be at risk of cystic fibrosis, then your doctor can conduct additional tests on your developing child.

See Also: Medicine Online Genetic testing isn’t for everyone. As you decide to be tested, you should talk to a genetic counselor about the psychological impact the test results might carry.

How to Teat Mucoviscidosis?

The treatment of� mucoviscidosis :

1. Preventing and controlling infections which occur in the lungs 2. Removing and loosening mucus from the lungs 3. Treating and preventing intestinal blockage 4. Providing adequate nutrition

Conclusion: Cystic fibrosis is a serious genetic condition which causes severe damage to the respiratory and digestive systems. In the above article, we have talked about cystic fibrosis its symptoms, causes, complications, risk factors, preventions and most importantly the treatment. If you feel and realize any of the above symptoms then consult a doctor as soon as possible.

Disclaimer: GoMedii is a recognized and a considerate healthcare platform which tends to connect every dot of the healthcare needs and facilities. GoMedii facilitates the accessibility of all health news, health tips, and information from the Health experts and Doctors to the eyes of readers. All of the information and facts mentioned in the GoMedii Blog are thoroughly examined and verified by the Doctors and Health Experts, elsewise source of information is confirmed for the same.