ectodermal dysplasia C D A J O U R N A L , V O L 4 9 , Nº 6
C.E. Credit
Interdisciplinary Approach for the Oral Rehabilitation of an Ectodermal Dysplasia Patient Konstantinos Chochlidakis, DDS, MS; Evangelia Lampraki, DDS; Maria Gabriela Carranza, DDS; Carlo Ercoli, DDS, MBA; Theocharis Nikellis, DMD; and Alexandra Tsigarida, DDS, MS
abstract Background: Ectodermal dysplasia is a rare genetic disorder with common oral and extraoral manifestations that require a medical-dental multidisciplinary approach. Case description: Dental treatment is often complex, includes treatment in both jaws, starts in early childhood and involves the coordination of multiple treatment phases and specialists. The surgical and prosthetic rehabilitation of an individual with ectodermal dysplasia is presented. Practical implications: Diagnostic and patient communication approaches, key treatment steps and prognostic indicators are emphasized in order to provide a clinically relevant protocol to the reader. Key words: Ectodermal dysplasia, rehabilitation, implants, restorations
AUTHORS Konstantinos Chochlidakis, DDS, MS, is an associate professor and program director in the department of prosthodontics at the Eastman Institute for Oral Health at the University of Rochester, N.Y. He is a fellow of the American College of Prosthodontists. Conflict of Interest Disclosure: None reported. Evangelia Lampraki, DDS, is a prosthodontist in private practice in Dubai, United Arab Emirates. She is a fellow of the American College of Prosthodontists. Conflict of Interest Disclosure: None reported.
Maria Gabriela Carranza, DDS, is an assistant professor at the Eastman Institute for Oral Health at the University of Rochester, N.Y. She is a fellow of the American College of Prosthodontists. Conflict of Interest Disclosure: None reported. Carlo Ercoli, DDS, MBA, is a professor of prosthodontics and periodontics and the chair of the department of prosthodontics at the Eastman Institute for Oral Health at the University of Rochester, N.Y. Conflict of Interest Disclosure: None reported.
Theocharis Nikellis, DMD, is a resident in the department of prosthodontics at the Eastman Institute for Oral Health at the University of Rochester, N.Y. Conflict of Interest Disclosure: None reported.
Alexandra Tsigarida, DDS, MS, is an associate professor and program director in the department of periodontics at the Eastman Institute for Oral Health at the University of Rochester, N.Y. Conflict of Interest Disclosure: None reported.
E
ctodermal dysplasia (ED) is a rare genetic disorder that affects the development and/ or homeostasis of two or more structures of ectodermal origin.1 Reported prevalence is contradictory but is estimated to be 1 in 5,000–100,000 births.1–3 Patients often present with a combination of clinical signs, such as nail malformations, hypotrichosis, sweat gland abnormalities, skin dryness and fragility and dentofacial malformations.1–5 The oral manifestations include dental abnormalities, such as anodontia, hypodontia or oligodontia and, especially in males, underdevelopment of the alveolar processes and tooth shape anomalies.2,3 The latter are often evident with conical or tapered shapes JUNE 2 0 2 1
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